From: Attenuated Ca2+ release in a mouse model of limb girdle muscular dystrophy 2A
 | Action potential amplitude (mV) | |||||||||||||||
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
10Â Hz | 20Â Hz | 50Â Hz | 100Â Hz | |||||||||||||
First AP | Last AP | First AP | Last AP | First AP | Last AP | First AP | Last AP | |||||||||
Strain | WT | C3KO | WT | C3KO | WT | C3KO | WT | C3KO | WT | C3KO | WT | C3KO | WT | C3KO | WT | C3KO |
Mean (±SEM) | 131.80 (±2.63) | 129.84 (±1.59) | 130.30 (±2.73) | 128.58 (±1.57) | 131.37 (±2.90) | 129.30 (±1.71) | 127.63 (±2.97) | 125.58 (±1.54) | 130.20 (±3.03) | 127.93 (±1.66) | 120.66 (±3.15) | 118.12 (±1.35) | 128.79 (±2.89) | 127.28 (±1.63) | 107.56 (±3.37) | 103.34 (±1.55) |
N | 14 | 18 | 14 | 18 | 14 | 18 | 14 | 18 | 13 | 18 | 13 | 18 | 13 | 18 | 13 | 18 |